- ( 95% ). () IX ().
. 6 : (Gower 1, Gower 2, Portland), (HbF), (1, 2). . 14-17.
14-17. ( .. , .. , 2001)
( ): 1 2. 1-2% F. HbF β-, β- (HbSS, S .), , . α- γ- β-. Hb2 ( 3,4%) β-, , 12 . Hb2 α-, .
, , , , , - (HbS), (Hb, HbEE, HbDD .).
. : (HbO2), - , ( , HbH), . , , . (, HbMet) (SHb), ( , , , .). 1%. HbMet, SHb 15% ( ). HbMet SHb, (HbCO), () (Ni(CO)4; Fe(CO)5), - , -
. , , , - - , 50% , - .